Objective: Paraesophageal hernias represent advanced degrees of slidin
g hiatus hernia with intrathoracic displacement of the intraesophageal
junction. Gastroesophageal reflux disease occurs in most cases, resul
ting in acquired short esophagus, which should influence the type of r
epair selected. Methods: Between 1960 and 1996, 94 patients with massi
ve, incarcerated paraesophageal hiatus hernia were operated on at the
Toronto General Hospital. The mean age was 64 years (39 to 85 years),
with a female to male ratio of 1.8:1. Organoaxial volvulus was present
in 50% of cases. Clinical presentation in these patients included pos
tprandial pain in 56%, dysphagia in 48%, chronic iron deficiency anemi
a in 38%, and aspiration in 29%. Symptomatic reflux, either present or
remote, was recorded in 83% of cases. All patients underwent endoscop
y by the operating surgeon. In 91 of 94 patients, the esophagogastric
junction was found to be above the diaphragmatic hiatus, denoting a sl
iding type of hiatus hernia. Gross, endoscopic peptic esophagitis was
observed in 36% of patients: ulcerative esophagitis in 22% and peptic
esophagitis with stricture in 14%. A complete preoperative esophageal
motility study was obtained for 41 patients. The lower sphincter was h
ypotensive in 21 patients (51%), and the amplitude of peristalsis in t
he distal esophagus was diminished in 24 patients (59%). These abnorma
lities are both features of significant gastroesophageal reflux diseas
e. In 13 recent, consecutive patients with paraesophageal hernia, the
distance between the upper and lower esophageal sphincters was measure
d during manometry. The average distance was 15.4 +/- 2.33 cm (11 to 2
0 cm), which is consistent with acquired short esophagus. The normal d
istance is 20.4 cm +/- 1.9 (p < 0.0001). Results: All 94 patients were
treated surgically: 97% had a transthoracic repair with fundoplicatio
n. A gastroplasty was added in 75 cases (80%) because of clearly defin
ed or presumed short esophagus. There were two operative deaths, and t
wo patients were never followed up. Among the 90 available patients, t
he mean follow-up was 94 months; median follow-up aas 72 months. Seven
ty-two patients (80%) are free of symptoms (excellent result); 13 (13%
) have inconsequential symptoms requiring no therapy (good result); an
d three patients (4%) are improved but have symptoms requiring medical
therapy or interval dilatation (fair result). Two patients had poor r
esults because of recurrent hernia and severe reflux. Both were succes
sfully treated by reoperation with the addition of gastroplasty becaus
e of acquired shortening, which was not recognized at the first operat
ion. Conclusions: Most of these 94 patients had symptoms or endoscopic
, manometric, and operative findings that were consistent with a slidi
ng hiatus hernia. There was a high incidence of endoscopic reflux esop
hagitis and of acquired short esophagus. True paraesophageal hernia, w
ith the esophagogastric junction in a normal abdominal location, appea
rs rare. Our observations were supported by measurements obtained at p
reoperative endoscopy and manometry, and by findings at the time of su
rgical repair. These observations support the choice of a transthoraci
c approach for repair in most patients.