RENDU-OSLER-WEBER-DISEASE - TRANSCATHETER EMBOLIZATION IN A PATIENT WITH PULMONARY ARTERIOVENOUS-FISTULAS

Authors
BRAGETTI P CASASCO A CAPUTO N HAMAM M MARTELLO C
Citation
P. Bragetti et al., RENDU-OSLER-WEBER-DISEASE - TRANSCATHETER EMBOLIZATION IN A PATIENT WITH PULMONARY ARTERIOVENOUS-FISTULAS, Rivista italiana di pediatria, 23(5), 1997, pp. 901-903
Citations number
9
Journal title
Rivista italiana di pediatria → ACNP
ISSN journal
03925161
Volume
23
Issue
5
Year of publication
1997
Pages
901 - 903
Database
ISI
SICI code
0392-5161(1997)23:5<901:R-TEIA>2.0.ZU;2-K
Abstract
A case of Rendu-Osler-Weber disease in a young girl is presented. The autosomial dominant disease with variable penetrance is characterized by multiple telengiactasic lesions and arteriovenous malformations (fi stulas) involving skin, mucous membrane, liver, lung and brain. The pa tient, with several pulmonary and cerebral arteriovenous fistulas and clinical signs of cronic hypoxia, was treated by transcatheter emboliz ation of larger pulmonary fistulas with ballons and tungesteno spirals , with good result.