THROMBOEMBOLIC STROKE, MOYA-MOYA PHENOMENON AND PRIMARY OXALOSIS

We present the clinical, radiological and autopsy findings in a 32-yea r-old woman with primary oxalosis, who suffered recurrent bilateral ca rotid territory infarcts. The overall features were those of moya-moya syndrome, with bilateral, ultimately thrombotic, occlusion of the dis tal internal carotid arteries. Vessel pathology suggests an underlying intimal vasculopathy, the possible relation of which to the patient's metabolic abnormality is discussed.