A case of malignant carotid body tumor with nodal, hepatic and bone me
tastases is reported. Carotid body chemodectomas are slow-growing tumo
rs which invade local structures. These tumors are usually benign but
can occasionally produce local and distant metastases. Development of
metastatic localizations is the only formal proof of malignancy as his
tology cannot distinguish between benign and malignant chemodectomas.
Bilateral carotoid arteriography gives the diagnosis. Surgery is the b
asis of treatment and should be performed early in the course to limit
operative complications. Radiotherapy can be given as adjuvant treatm
ent.