L. Crenier et al., A CASE OF RAPIDLY FATAL SYSTEMIC CAPILLARY LEAK SYNDROME IN A KIDNEY-TRANSPLANT RECIPIENT, Acta Clinica Belgica, 52(6), 1997, pp. 401-404
Idiopathic Systemic Capillary Leak Syndrome (SCLS) is a rare entity ch
aracterised by idiopathic increasing of capillary permeability associa
ted with recurrent attacks of hypovolaemic shock. We report the case o
f a 39-year-old man with a SCLS fourteen years after a cadaveric renal
transplantation. The clinical evolution was rapidly fatal despite tre
atment with corticoids, aminophylline and terbutaline which are the mo
st efficient drugs known to prevent attacks.