CYSTIC-FIBROSIS - AN OVERVIEW

Authors
Citation
C. Ruzalshapiro, CYSTIC-FIBROSIS - AN OVERVIEW, The Radiologic clinics of North America, 36(1), 1998, pp. 143
Citations number
48
Categorie Soggetti
Radiology,Nuclear Medicine & Medical Imaging
ISSN journal
00338389
Volume
36
Issue
1
Year of publication
1998
Database
ISI
SICI code
0033-8389(1998)36:1<143:>2.0.ZU;2-B
Abstract
A single gene defect in cystic fibrosis results in a spectrum of clini cal presentations. Though expression is variable, the radiographic app earance reflects the underlying pathophysiology. Abnormalities of the small airways result in air-trapping; bronchiectasis and mucus pluggin g reflect large airway disease. These radiographic findings can be ass essed and followed using varying scoring systems.