Purpose We present preliminary research on penetrating keratoplasty in
corneal dystrophy secondary to congenital Thf aim was To analyse rhp
functional and anatomic results of this morbid condition where visual
prognosis is usually poor. Patients and methods Six cases of congenita
l glaucoma in which the ocular pressure is controled were studied. Age
varied from 10 months to 11 years, the medium age was 47.7 months (SD
: 42.8). These patients underwent penetrating keratoplasty, Recession
varied from 3 months to 29 months, with a medium recession of 18.4 mon
ths (SD: 11.54). Results Anatomic results: the graft remained transpar
ent in 5 eyes. Some postoperative complications were noticed: ocular h
ypertonia medically treated in one case, minor uveitis in one case, to
tal cataract operated by hypertonia with a final outcome of ophthalmom
alacia, buphtalmia (31.5 of diameter and ocular tonus at 7 mmHg). Func
tional results: on amelioration elf visual acuity was obtained in 5 of
6 cases. Conclusion The anatomic and functional results were satisfac
tory. Ocular pressure must be normalised before keratoplasty. Importan
t buphtalmia constitutes one contra-indication ro this intervention. H
ypotonia would appear To be a factor of poor prognosis.