While small-bowel transplantation remains an option for the management
of short-bowel syndrome (SBS), every effort must be made to optimize
the function of the native bowel. This report describes a patient with
SBS who dramatically improved after a Bianchi procedure. The patient
was born with type IIIb jejunal atresia, complicated by volvulus of th
e terminal ileum. He was left with 40 cm of small bowel and his ileoce
cal valve. During the first 20 months of his life, he was always hospi
talized except for 3 months. He was on parenteral nutrition (TPN) and
suffered multiple episodes of central line sepsis. Massive small-bowel
dilatation caused a functional bowel obstruction with bacterial overg
rowth, and villous atrophy of the jejunal mucosa was discovered on bio
psies done by colonoscopy. In March 1994, we elected to proceed with a
Bianchi procedure. Thirty cm of jejunum were divided longitudinally.
During the following year, his enteral tolerance steadily improved to
the point where TPN could be discontinued.