A Behcet's disease patient developed sudden cochlear hearing loss duri
ng a flare of her disease. Prednisone and cyclosporin therapy was inef
fective, probably because it was initiated late. Sensorineural hearing
loss is a rare but underrecognized complication of various forms of v
asculitis such as Wegener's granulomatosis, polyarteritis nodosa, gian
t cell arteritis and Behcet's disease. Its importance lies in the need
for an early diagnosis, since prompt treatment with steroids and immu
nosuppressive agents may lead to restoration of hearing.