A case of a hereditary sensory autonomic neuropathy (HSAN) with severe
medical complications that had been reported as nonprogressive HSAN t
ypo II has been followed and treated for a period of 10 years, and is
now considered to be progressive HSAN type III, is presented, Current
difficulties in the present form of the classification of HSAN, the ne
cessity to observe these cases for longer periods and possible prolong
ation of survival with appropriate supportive treatment are emphasized
.