RESULTS OF TYMPANOPLASTY IN CHILDREN WITH PRIMARY CILIARY DYSKINESIA

Objective: To assess the results of tympanoplasty in children with pri mary ciliary dyskinesia complicated by tympanic perforation or cholest eatoma with hearing loss and/or recurrent otorrhea. Design: Retrospect ive study. Postoperative follow-up of 26.3 months in the type 1 tympan oplasty group and 46 months in the child with cholesteatoma. Setting: Hospitalized care, referral center. Patients: Seven children with prim ary ciliary dyskinesia, complicated in 6 children by 9 tympanic perfor ations (3 bilateral perforations) and in 1 child by an attical cholest eatoma. Results: After 9 type 1 tympanoplasties, the grafts were intac t in 9 ears, with no recurrence of otorrhea, but serous otitis media w as present in 6 of the 9 ears. Auditory improvement was significant, w ith an average gain of 17-dB hearing level in speech frequencies. Afte r a canal wall-down tympanoplasty with mastoidectomy for attic cholest eatoma in 1 ear, the cavity that was operated on showed no signs of ot orrhea or residual cholesteatoma after a follow-up of 46 months. Concl usion: In children with primary ciliary dyskinesia, tympanoplasty has a high probability of graft success and auditory improvement, despite the frequent recurrence of serous otitis media.