RIGHT-VENTRICULAR ANEURYSM ASSOCIATED WITH ADVANCED HYPERTROPHIC CARDIOMYOPATHY

A previously undescribed case of right ventricular aneurysm (RVA) asso ciated with hypertrophic cardiomyopathy in an advanced stage is report ed. The diagnosis was established by noninvasive (cardiac two-dimensio nal echocardiogram and nuclear MRI) adn invasive (cardiac catheterizat ion, angiography, and biventricular endomyocardial biopsy) cardiac exa minations, which documented hypertrophied, dilated and hypokinetic biv entricular chambers associated with typical histologic findings (histo logic hypertrophic cardiomyopathy index of 66%). A prominent narrowing of myocardial arterioles, extended to the right ventricular myocardiu m, has been identified and has been hypothesized as being responsible for RVA formation.