A case of solitary osteoma of the parietal skull is described in a mot
her and her 12-year-old son. There were no other craniofacial or dysmo
rphic features and there was no history of previous cranial trauma or
inflammatory process and no radiographic evidence of other skeletal le
sions in both patients. Family history was otherwise unremarkable. Gar
dner syndrome was ruled out by excluding other associated clinical abn
ormalities and by family history. The clinical and radiological featur
es of the patients' osteomas were different from those of Albright her
editary osteodystrophy, fibrodysplasia ossificans progressiva, progres
sive osseous heteroplasia and familial ectopic ossification. To the au
thor's knowledge this is the first case of the familial presentation o
f osteomas.