P. Lapinski et al., SPORADIC DYSTROPHIC EPIDERMOLYSIS-BULLOSA WITH CONCOMITANT ATOPIC-DERMATITIS, British journal of dermatology, 138(2), 1998, pp. 315-320
We describe a patient with sporadic dystrophic epidermolysis bullosa a
ssociated with well-documented atopic dermatitis. We discuss this case
in relation to a newly described clinical subtype of epidermolysis bu
llosa known as epidermolysis bullosa pruriginosa, a dystrophic variant
associated with prominent pruritus. The relations of this case of spo
radic dystrophic epidermolysis bullosa with other dominantly inherited
forms of dystrophic epidermolysis bullosa such as the Pasini variant,
the pretibial variant, and Bart's syndrome are also discussed, The ro
le of atopic dermatitis in exacerbating dystrophic epidermolysis bullo
sa in this patient raises an important consideration in the care of th
is group of patients.