SPORADIC DYSTROPHIC EPIDERMOLYSIS-BULLOSA WITH CONCOMITANT ATOPIC-DERMATITIS

We describe a patient with sporadic dystrophic epidermolysis bullosa a ssociated with well-documented atopic dermatitis. We discuss this case in relation to a newly described clinical subtype of epidermolysis bu llosa known as epidermolysis bullosa pruriginosa, a dystrophic variant associated with prominent pruritus. The relations of this case of spo radic dystrophic epidermolysis bullosa with other dominantly inherited forms of dystrophic epidermolysis bullosa such as the Pasini variant, the pretibial variant, and Bart's syndrome are also discussed, The ro le of atopic dermatitis in exacerbating dystrophic epidermolysis bullo sa in this patient raises an important consideration in the care of th is group of patients.