A rare case of peliosis hepatis associated with idiopathic restrictive
cardiomyopathy is reported, A 75-year-old man was admitted for evalua
tion of marked edema and jaundice, Serum total bilirubin was elevated
above 20 mg/dl, The liver biopsy under laparoscopy revealed marked sin
usoidal dilatation and retention of red blood cells, which was consist
ent with a diagnosis of peliosis hepatis, Cardiac catheterization reve
aled right ventricular filling disturbance without specific findings o
n endomyocardial biopsy, suggesting idiopathic restrictive cardiomyopa
thy. The level of serum total bilirubin decreased in association with
improvement of edema after drip infusion of furosemide therapy.