Aims: We describe the clinical and pathological findings of a previous
ly unreported cutaneous lung tissue heterotopia in a child. Case detai
ls: The 3-year-old female patient developed a 8-mm secreting papule ov
er her left scapula, Pathological examination revealed a lesion compos
ed of bronchioles and alveoli within the subcutis and the dermis. with
bronchiolar connection to the epidermis. Alveolar type II cells indic
ating full pulmonary differentiation were detected with a monoclonal a
ntibody (AMH 152). Conclusions: The described features suggest that th
is lesion is a unique variant of rarely observed bronchus-like entitie
s of the skin, designated as cutaneous bronchogenic cysts or cutaneous
branchial cleft cysts.