MOYAMOYA DISEASE IN A PATIENT WITH HEREDITARY SPHEROCYTOSIS

Moyamoya disease (MMD) is a rare cerebral vasculopathy characterized b y occlusion of the supraclinoid portion of the internal carotid artery and proximal portions of the anterior and middle cerebral arteries. P atients develop an extensive collateral network of parenchymal, transd ural and leptomeningeal vessels to supply the compromised brain. These collateral channels, also known as ''moyamoya vessels,'' may be seen in a number of disorders which lead to intracranial vascular occlusion . We report a case of MMD in a child with hereditary spherocytosis.