A respirator-dependent 11-day-old boy with Ebstein's anomaly is presen
ted. His cardiac anomaly with progressive cardiomegaly was first notic
ed at 24 weeks' gestation on fetal echocardiography. After birth, he r
equired mechanical ventilation because of massive tricuspid regurgitat
ion and restricted pulmonary blood flow. The operation of tricuspid va
lve patch closure, resection of right atrial wall, and central shunt s
uccessfully weaned him from the respirator on postoperative day 13. Ca
vopulmonary anastomosis was performed without problem when the patient
was 8 months of age. (C) 1998 by The Society of Thoracic Surgeons.