NEVOID BASAL-CELL CARCINOMA SYNDROME IN A BLACK-CHILD

Nevoid basal cell carcinoma syndrome (NBCCS) is rare in black persons, We describe an 11-year-old black boy with NBCCS who presented with ex otropia and a painful, expanding, cystic mass in the left posterior al veolar ridge, Further examination revealed odontogenic keratocysts wit h palmar and plantar pitting. Less than 5% of reported patients with N BCCS are black. To our knowledge, this is the first report of a black patient with NBCCS presenting with exotropia and an impacted molar dis placed into the orbit by an odontogenic keratocyst.