Two female infants with callosal agenesis, infantile spasms, chorioret
inal lacunae, optic disc colobomas and cortical heterotopias were diag
nosed with Aicardi syndrome. A choroid plexus papilloma was found in o
ne patient, and choroid plexus cysts were found in the other. Choroid
plexus lesions are common findings in the Aicardi syndrome and are dis
cussed in this paper.