PETERS ANOMALY ASSOCIATED WITH PROTRUDING CORNEAL PSEUDO STAPHYLOMA

Purpose. To describe a new manifestation of Peters' anomaly. Methods. We managed four infants with an unusual form of Peters' anomaly. One e ye of each patient had a thickened and scarred cornea, mimicking a cor neal staphyloma, protruding anteriorly from the corneal plane. The oth er eye of each patient ranged from normal to having severe ocular anom alies. A corneal transplant was performed in each case. Results. Follo w-up ranged from 1 to 3 years. Three eyes maintained graft clarity for at least 1 year. Each of these eyes developed vision. Two of these ey es developed glaucoma. The one eye with graft failure developed an ino perable retinal detachment. The histopathology of each corneal burton showed changes consistent with Peters' anomaly. Conclusions. These cor neas demonstrated characteristics of both Peters' anomaly and congenit al anterior staphyloma. Despite their severe anomalies, surgery succes sfully restored a more normal cosmetic appearance in all four eyes and vision in three eyes.