The association of sensorineural hearing loss and ulcerative colitis i
s well documented and it is speculated that this is autoimmune in orig
in. A case in a 12-year-old boy is described, that initially responded
to steroid therapy, but four years later resulted in bilateral, profo
und sensorineural hearing loss in spite of good control of his bowel d
isease. Immunological tests may provide a clue as to the aetiology of
suspected cases of autoimmune inner ear disease. Immediate treatment w
ith steroids with or without immunosuppressive therapy is essential as
delay may lead to irreversible hearing loss.