MONSTROUS SKULL OSTEOMAS IN A PROBABLE GARDNERS-SYNDROME - CASE-REPORT

BACKGROUND Gardner's syndrome includes a clinical triad of familial po lyposis coli, osteomas, and soft tissue tumors. METHODS We present a v ery unusual case of probable isolated Gardner's syndrome characterized by extremely voluminous osteomas in the occipital and frontal areas a ssociated with diffuse subcutaneous lipomas and without colic abnormal ity. RESULTS The neurosurgical management included resection of the os teomas for cosmetic reasons. After a follow-up period of 5 years, the patient remains free of digestive complaints and the resected osteomas did not recur. CONCLUSIONS The special clinical presentation of our c ase of possible Gardner's syndrome is discussed. (C) 1998 by Elsevier Science Inc.