TREATMENT OF PRUNE-BELLY-SYNDROME AT ABID JAN-UNIVERSITY-HOSPITAL (TREICHVILLE)

Over the past 10 years, we have seen sixteen children (15 males and 1 female) with the prune-belly syndrome. We have managed 12 of these chi ldren, but 4 of them were never reviewed, Abdominal wall reconstructio n was performed in 11 children by dissection of spermatic vessels and fixing the testis in the scrotum. Because of our conservative approach to the management of urinary tract dilatation, we performed only one nephrostomy and 3 unilateral nephro-ureterectomies. Seven children wer e reviewed, The result of abdominal wall reconstruction was good in te rms of cosmetic appearance and psychologic effect for the parents; we have observed no atrophic testes after orchidopexy. One of these child ren suffers from chronic renal failure, while the other children have good renal function. Prune-belly syndrome is a disease with a broad sp ectrum. The prognosis depends on the degree of renal dysplasia. These children require long-term follow-up.