A 67-year-old male patient presented with a nephrotic syndrome. Biopsy
of the kidney revealed the characteristic of fibrillary glomerulopath
y on light and electron microscopy. Other non-nephritic causes of a ne
phrotic syndrome (e.g. amyloidosis, immunotactoid glomerulopathy, ligh
t-chain glomerulopathy, cryoglobulinaemia, collagen-ill glomerulopathy
, fibronectin glomerulopathy) could be excluded. Besides the case repo
rt, differential diagnosis of fibrillary glomerulopathies is presented
.