BEHAVIORAL-MANAGEMENT OF PRADER-WILLI-SYNDROME

Prader-Willi syndrome is a genetic illness associated with a defect on chromosome 15. It presents with hypotonicity in infancy followed by v oracious appetite and gross obesity from early childhood and with a ra nge of other clinical and behavioural sequelae. This case report is of an adolescent boy who was admitted to a psychiatric unit for an inten sive behavioural programme to control his weight gain and deal with as sociated behavioural problems, and demonstrates that an inpatient prog ramme can lead to sustainable improvements in weight control and other indicators of well-being in PWS patients.