MIDDLE AORTIC SYNDROME IN A BOY WITH ARTERIOHEPATIC DYSPLASIA (ALAGILLE-SYNDROME)

Middle aortic syndrome is increasingly recognized as a cause of hypert ension in adolescents and young adults. Alagille syndrome is a genetic disorder characterized by hepatic, eye, and bony abnormalities, Cardi ovascular lesions occur in most of the patients, but narrowing of the abdominal aorta has not been previously recorded, We present an unusua l association between middle aortic syndrome and Alagille syndrome, wi th a similar vascular lesion seen In two generations.