Epignathus is an extremely rare form of teratoma that arises from the
palate or pharynx in the region of the basisphenoid (Rathke's pouch).(
4) This condition is associated with a high mortality rate caused by s
evere airway obstruction in the neonatal period, thus requiring prenat
al planning and prompt surgical treatment after birth. The authors des
cribe a case of giant epignathus that was successfully resected follow
ed by an uneventful recovery. Copyright (C) 1998 by W.B. Saunders Comp
any.