A case of split notochord syndrome associated with a prolapsed colosto
mylike dorsal enteric opening, a foreshortened colon, imperforate anus
, and meningocele is presented. The surgical management of this disord
er is discussed and available literature reviewed. The patient was suc
cessfully treated with a combined, single-stage surgical correction. C
opyright (C) 1998 by W.B. Saunders Company.