Oligodontia is defined as the congenital absence of six or more teeth,
excluding the third molars. Genetic factors play an important role in
oligodontia, which can occur as an isolated finding or as part of a s
yndrome. Characteristic dental symptoms are a reduced number of teeth,
a reduction in tooth size, anomalies of tooth form, and delayed erupt
ion. This article describes treatment of a 6-year-old girl with congen
ital absence of 16 permanent teeth. Her malocclusion was corrected by
orthodontic therapy, and removable partial dentures were made to impro
ve esthetics and chewing function.