STURGE-WEBER SYNDROME WITH NO LEPTOMENINGEAL ENHANCEMENT ON MRI

Sturge-Weber syndrome (SWS) is a neurocutaneous syndrome characterized by a facial nevus flammeus associated with seizures, developmental de lay, and, often, with hemiparesis and hemi anopia. On MRI, the most ch aracteristic finding has been reported to be leptomeningeal enhancemen t, believed to represent leakage of contrast medium through the anomal ous pial vessels that characterize the disease. We present a case of S WS with no evidence of leptomeningeal enhancement. This case illustrat es that leptomeningeal enhancement need not be present in SWS, and the absence of this characteristic finding does not preclude the diagnosi s.