URINARY HYDROCOLPOS, CLOACAL MALFORMATION AND PRE-AXIAL POLYDACTYLY -A RARE VARIANT OF NEONATAL HYDROCOLPOS

Hydrocolpos is characterized by a vaginal obstruction with cystic dila tation of the vagina. The latter is usually caused by accumulation of cervical and endometrial mucus but in rare instances urine is accumula ted through a vesicovaginal fistula proximal to the obstruction. Hydro colpos and hydrometrocolpos may be associated with other malformations , such as postaxial polydactyly, anal atresia, esophageal atresia, ren al agenesis, genital anomalies, and cardiopathy. Each neonate presenti ng with hydrocolpos should be evaluated for other clinically silent ma lformations, such as hamartoblastoma of the hypothalamic region. We re port a patient with urinary hydrocolpos and cloacal malformation; it i s the first case of hydrocolpos with pre-axial polydactyly. We briefly describe embryogenesis of the different types of vaginal obstruction and discuss prenatal and neonatal diagnosis and differential diagnosis .