Primary pulmonary amyloidosis is a rare disorder that appears in three
forms. tracheobronchial? nodular parenchymal, and diffuse parenchymal
. We report the case of a 46-year-old women with extensive tracheobron
chial amyloidosis which presented with a 2-year history of dyspnea and
with signs of severe fixed obstruction in pulmonary function tests. C
omputed tomography of the thorax demonstrated marked thickening of the
trachea and the central bronchial tree with substantial narrowing of
the main, lobar, and segmental bronchi. Transbronchial specimen showed
typical birefringence under polarizing microscope after staining with
Congo Red. We did not find hints for systemic amyloidosis.