M. Kourda et al., GIANT-CELL FIBROBLASTOMA ASSOCIATED WITH DERMATOFIBROSARCOMA PROTUBERANS OF THE ADULT, Annales de dermatologie et de venereologie, 125(4), 1998, pp. 255-256
Introduction. Giant cell fibroblastoma is a rare mesenchyma tumor of c
hildhood having many similarities with dermatofibrosarcoma protuberans
in adults. Observation. We report the case of a 28-year-old woman pre
senting a subcutaneous inter-mammary mass associating both tumors. Imm
unohistochemistry showed an expression of CD 34 only by dermatofibrosa
rcoma protuberans cells. Discussion. It is important to stress: the ra
rity of this association, the difficulty to confirm the diagnosis and
to establish the links between these two tumors : simple association (
as in our case), transformation or recurrence of giant cell fibroblast
oma in dermatofibrosarcoma protuberans.