Teratoma with malignant transformation is defined as the emergence of
a non-germ cell tumor from a teratoma. Although extremely rare in extr
aovarian sites, cases have been reported that involve primary extragon
adal germ cell tumors with transformation to variants of sarcoma. We r
eport a 54-year-oid man who was found to have adenocarcinoma arising w
ithin a mature teratomatous retroperitoneal metastasis 15 years after
treatment of a nonseminomatous testicular germ cell tumor. The tumor w
as successfully excised and he remains without evidence of disease. (C
) 1998, Elsevier Science Inc. All rights reserved.