Although the most common form of nasal obstruction in neonates is soft
tissue edema, congenital bony nasal deformities are being recognized
as an important cause of newborn airway obstruction. In addition to th
e well described choanal atresia, CT imaging of the newborn in respira
tory distress reveals two other forms of bony nasal cavity deformities
: nasal pyriform aperture stenosis and nasal cavity stenosis. All of t
he three types of bony nasal cavity deformities have characteristic an
atomical features, are associated with distinctive congenital anomalie
s, and are postulated to have differing embryological causes. Five pat
ients with congenital bony nasal cavity deformities ave presented. The
se cases illustrate the clinical and radiological presentation of vari
ed types of congenital nasal cavity obstruction as well as the criteri
a used to guide clinical management.