Objectives. 1. To ascertain the causes of severe visual impairment and
blindness in children in schools for the blind in South Africa. 2. To
determine the major avoidable causes. 3. To determine causation by et
hnic group. Design. A cross-sectional survey undertaken at 15 of the 1
6 schools for the blind in South Africa, during May September 1996, us
ing standard WHO methodology. Subjects. Children less than 16 years of
age on May 1996. Results, Of 1615 eligible children, 1311 were examin
ed, According to WHO categories of visual impairment, using the correc
ted visual acuity in the better eye, 30.4% of children were blind (< 3
/60, BL), 12.6% had severe visual impairment:(< 6/60 - 3/60, SVI), 42.
3% were visually impaired (< 5/18 - 6/60), and 12.0% had no impairment
(6/18 or better). The anatomical sites of SVI/BL in 564 children were
: retina 38.5%; optic nerve 15.2%; cornea/phthisis bulbi 11.0% and gla
ucoma 6.7%. Aetiological categories of SVI/BL were: hereditary disease
s 33.0%; intra-uterine factor; 0.9%; perinatal conditions 13.1%; acqui
red conditions of childhood 11.5%, In 41.5% the underlying cause could
not be determined. In 38.8% of children with SVI/BL the cause was avo
idable, i.e. preventable or treatable. The main causes varied between
ethnic groups, the major difference being the higher proportion of ret
inopathy of prematurity in white and Indian children. Conclusions. The
study suggests that 38.8% of causes of SVI or blindness in children i
n schools for the blind in South Africa are avoidable, and that specif
ic control measures need to be targeted at different ethnic groups.