PRIMARY CRANIAL EWINGS-SARCOMA

Primary Ewing's sarcoma of the cranium is extremely rare, with only 17 cases reported so far. We describe a further case with involvement of the frontotemporal region and the orbit. The patient, an adult male, was admitted with headache and papilloedema, and later developed local ised swelling and proptosis. He was treated with surgery, radiotherapy and chemotherapy, and was free from metastases during a follow-up of 14 months. The prognosis of Ewing's sarcoma is improving with radiothe rapy and chemotherapy. Further cases are needed to study the biologica l behaviour of primary cranial Ewing's sarcoma.