A newborn with an unusual form of truncus arteriosus is described, who
se clinical presentation and certain features of her anatomy were more
typical of pulmonary atresia with a ventricular septal defect. The mo
rphological differentiation of certain types of truncus arteriosus and
pulmonary atresia with ventricular septal defect remains an area of s
peculation among cardiac pathologists, and research in this area is be
ing done using animal models. The anatomic features of the heart descr
ibed in this report may assist in this discussion as the application o
f observations made in animal models to human cardiac development may
be problematic.