PYOSTOMATITIS VEGETANS IN CHILDHOOD

Pyostomatitis vegetans is an oral eruption, characterized by small pus tules, ulcers and erythematous vegetations of the labial and buccal mu cosae as well as labial-attached gingivae. Its importance lies in its high correlation with inflammatory bowel disease. It is commonly assoc iated with skin and inflammatory bowel disease and is rare in children . We here report a sister and brother with onset of the disease at the age of 5 and 7 years, respectively. It is the first report of familia l pyostomatitis vegetans occurring in the youngest patients hitherto r eported. Conclusion The observation of two sibs with pyostomatitis, ve getans pyoderma gangrenosum and inflammatory bowel disease suggest a h ereditary disposition to this rare triad.