RELATION BETWEEN DIETARY-INTAKE AND NUTRITIONAL-STATUS IN CYSTIC-FIBROSIS

This study evaluated adherence to current dietary recommendations of c hildren with cystic fibrosis and mild lung disease and their siblings by comparing energy intake. Fifty children (25 with cystic fibrosis) a ged between 7 and 12 years completed the study. Energy intake was asse ssed by weighed dietary intake, resting energy expenditure was used to calculate recommended daily intakes. The children with cystic fibrosi s had significant deficits in Z scores for both height and weight comp ared with their siblings, but there was no difference in percentage of ideal weight for height. The cystic fibrosis group had a significantl y higher energy intake per kilogram body weight per day but there was no difference in the percentage of energy derived from fat, protein or carbohydrate. Energy intake (per kg/day) and fat intake (g/kg) were b oth significant predictors of weight for height in the cystic fibrosis group. Targets for dietary management in cystic fibrosis should perha ps be related to fat intake per kilogram body weight.