A 24-year-old man presented with hypertension, palpitations, and prema
ture atrial and ventricular contractions. A mass was discovered in the
distal interventricular septum that was composed of dense collagenous
tissue, fat, and disorganized, hypertrophic, mature cardiac myocytes
indicative of a cardiac hamartoma This entity has only rarely been rep
orted and must be distinguished from the much more common rhabdomyoma
and from oncocytic cardiomyopathy, which is also referred to as ''card
iac hamartoma''.