Purpose Brown's syndrome is a form of anatomical strabismus, or retrac
tion syndrome. It is defined by active and passive limitation of upwar
d gaze in adduction in the field of action of the inferior oblique mus
cle. The etiology of Brown's syndrome remains unknown. The defect lies
at the level of the superior oblique's tendonis trajectory via the tr
ochlea. We studied the frequency of clinical signs and results after s
urgery in patients presenting congenital Brown's syndrome. Patients an
d methods Our study involved 18 children. They all underwent complete
ophthalmological examination with orthoptic testing, pre and postopera
tively. Results Neither sidedness nor predominance of sex was noted. C
ompensatory head posture was noted in 7 of 18 cases, Limitation of upw
ard gaze in adduction was a constant finding, with a positive duction
rest. Eleven cases underwent superior-oblique recession. Results of su
rgery were satisfactory, with resolution of compensatory head posture
in over 80% of cases. Conclusion The etiology of congenital Brown's sy
ndrome remains unknown, The different surgical techniques give inconst
ant results. Operative indication is decided only when in the presence
of well defined clinical manifestations : CHP, deviation in primary p
osition with alteration of binocular vision.