DUPLICATION OF THE PITUITARY-GLAND IN A NEWBORN WITH MEDIAN CLEFT FACE SYNDROME AND NASAL

Authors
HAMONKERAUTRET M ARES GS DEMONDION X ROULAND V FRANCKE JP PRUVO JP
Citation
M. Hamonkerautret et al., DUPLICATION OF THE PITUITARY-GLAND IN A NEWBORN WITH MEDIAN CLEFT FACE SYNDROME AND NASAL, Pediatric radiology, 28(5), 1998, pp. 290-292
Citations number
3
Categorie Soggetti
Radiology,Nuclear Medicine & Medical Imaging",Pediatrics
Journal title
Pediatric radiology → ACNP
ISSN journal
03010449
Volume
28
Issue
5
Year of publication
1998
Pages
290 - 292
Database
ISI
SICI code
0301-0449(1998)28:5<290:DOTPIA>2.0.ZU;2-F
Abstract
A newborn suffered immediate neonatal respiratory distress because of an obstructive, soft-tissue nasal mass. Clinical examination revealed a cleft palate with a protruding polypoid mass. CT and MRI showed a he terogeneous nasopharyngeal mass and associated intracranial abnormalit ies-duplication of the hypophysis and hypoplasia of the corpus callosu m. Duplication of the hypophysis is a very rare malformation, only 13 cases having been previously described. The suggested pathogenesis is duplication of the prechordal plate and anterior end of the notochord during early embryological development.