We report a 3-year, 5-month-old boy with an adrenocortical carcinoma.
These tumours are rare and highly malignant in childhood. In most case
s they are functional, secreting adrenocortical hormones. In this case
there was a misleading coexistence with a second abdominal neoplasm,
which was a ganglioneuroma; this is a rare benign tumour arising from
the sympathetic nervous system. The imaging investigations and their f
indings are discussed and correlated with pathology.