Kp. Nzi et al., A CASE OF ASPLENIA IN A PATIENT WITH SS H OMOZYGOUS SICKLE-CELL DISEASE, Bulletin de la Societe de pathologie exotique et de ses filiales, 91(2), 1998, pp. 156-157
One case of total splenic atrophy is reported in a patient with SS hom
ozygous sickle-cell disease presenting no related malformation thus re
calling the IVEMARK syndrome. An abdominal echography and computed tom
ography are indispensable in order to confirm the absence of the anato
mic spleen; this makes for a better follow-up of sickle-cell disease.