A case of adult onset myopathy who showed a peculiar sleep-related res
piratory disorder (SRRD) is reported. She recovered from respiratory f
ailure after tracheostomy and/or with the aid of the respirator used o
nly during the night. Sleep study without the use of respirator reveal
ed that her sleep was highly fragmented by frequent arousal responses
due to inspiratory effort but not by apnea or hypopnea. To our knowled
ge this type of SRRD has not been described.