BERNARD-SOULIER-SYNDROME IN PREGNANCY - CASE-REPORT AND REVIEW OF THELITERATURE

Bernard-Soulier Syndrome is a rare hereditary thrombocytopathy that ma nifests clinically by excessive bleeding out of proportion to the degr ee of thrombocytopenia. Only eight reports of Bernard-Soulier Syndrome in pregnancy have been previously described. In some patients the pre gnancy course was smooth while in others post-partum haemorrhage was t he most common complication. We present a primiparous female who had i mmediate and delayed post-partum haemorrhage that was managed conserva tively. Review of the literature is also included.