O. Witt et al., Severe cerebral venous sinus thrombosis and dural arteriovenous fistula inan infant with protein S deficiency, CHILD NERV, 15(2-3), 1999, pp. 128-130
A 12-month-old infant presented with cerebral seizures and neurological def
icits. MRI scan of the brain and angiography showed massive-cerebral venous
sinus thrombosis complicated by a dural arteriovenous fistula. Subsequent
clotting analysis revealed a protein S deficiency. Screening for inherited
coagulation inhibitor deficiency is recommended in children with unexplaine
d or atypical thrombotic events.