We report the first case of vulvar porokeratosis that occurred in a 39-year
-old woman with a 30-year history of vulvar pruritus and disfiguring vulvar
lesions. Ultrasonic surgical aspiration resulted in resolution of her prur
itus and excellent cosmesis. Light microscopy revealed characteristic corno
id lamellae and electron microscopy confirmed the diagnosis of vulvar porok
eratosis.